Amniotic band associated with human tail-like cutaneous appendage and spinal dermoid tumor: An exceedingly rare triad

Authors

  • Leopoldo Mandic Ferreira Furtado Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil https://orcid.org/0000-0001-9472-9895
  • José Aloysio da Costa Val Filho Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil https://orcid.org/0000-0003-3261-7147
  • Bruno Lacerda Sandes Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil
  • Gustavo Alberto Rodrigues da Costa Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil
  • Fernando Levi Alencar Maciel Federal University of Vale do Jequitinhonha and Mucuri, Minas Gerais, Brazil
  • Eustaquio Claret dos Santos Júnior Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

DOI:

https://doi.org/10.29327/apn.v2i1(January-April).14

Keywords:

Amniotic band, Caudal appendage, Dermoid tumor, Spinal dysraphism

Abstract

Introduction: The association between amniotic band syndrome (ABS) and spinal dysraphism is an extremely rare entity that was paucity reported in the literature so far and similar conditions such multiple asymmetric encephaloceles and anencephaly were also previously described with ABS.

Methods: In this case report, we described a male newborn in whom ABS was associated with human tail and lumbar dysraphism. A surgical approach was performed with intraoperative neurophysiological monitoring in which the tail and amniotic band were en bloc resected with favorable outcome. Dermoid tumor was identified by histopathological analysis

Conclusion: The occurrence of spinal dysraphism combined with ABS should be managed carefully in order to avoid spinal cord damage. provides very good results for a number of indications in children. Every effort should be made to optimize the selection of surgical candidates on the basis of their clinical features.

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Author Biographies

Leopoldo Mandic Ferreira Furtado, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

Department of Pediatric Neurosurgery, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

José Aloysio da Costa Val Filho, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

Department of Pediatric Neurosurgery, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

Bruno Lacerda Sandes, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

Department of Pediatric Neurosurgery, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

Gustavo Alberto Rodrigues da Costa, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

Department of Pediatric Neurosurgery, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

Fernando Levi Alencar Maciel, Federal University of Vale do Jequitinhonha and Mucuri, Minas Gerais, Brazil

Faculty of Medicine, Federal University of Vale do Jequitinhonha and Mucuri, Minas Gerais, Brazil

Eustaquio Claret dos Santos Júnior, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

Department of Pediatric Neurosurgery, Vila da Serra Hospital, Nova Lima, Minas Gerais, Brazil

Additional Files

Published

2020-04-01 — Updated on 2020-04-01

How to Cite

1.
Furtado LMF, Val Filho JA da C, Sandes BL, da Costa GAR, Maciel FLA, dos Santos Júnior EC. Amniotic band associated with human tail-like cutaneous appendage and spinal dermoid tumor: An exceedingly rare triad. Arch Pediatr Neurosurg [Internet]. 2020 Apr. 1 [cited 2024 Apr. 18];2(1(January-April):49-52. Available from: https://archpedneurosurg.com.br/sbnped2019/article/view/14

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