What the time has taught about Hyperteleorbitism





Hyperteleorbitism, orbital hypertelorism, frontonasal dysplasia, frontoethmoidal meningoencephalocele, rare facial cleft


Introduction: Hypertelorbitism is a clinical feature that may be present in various types of pathologies and  degrees of manifestation. Observing the evolution of techniques over time and understanding the specific characteristics of each case demonstrates the difficulty of establishing treatment protocols.

Material and method: Retrospective analysis of over 150 cases of hypertelorbitism operated on over 44 years by the main author. The increased interorbital distance had varied etiologies: dysplasia, meningoencephaloceles, and dysostosis. 

Results: Retrusion of the facial middle third throughout growth in congenital hypertelorbitism was present in both dysplasia and dysostosis groups. In cases of early treatment with Tessier's glasses osteotomy there was zygomaticmaxillary atrophy with trapping of tooth germs. The cases of grade III and IV Hyperteleorbitism, with or without meningoencephalocele, which were treated without concomitant skullcap expansion, evolved to endocranial hypertension and required further treatment. Retrospective evaluation of their CT scans revealed craniosynostosis of one or more sutures, associated with predominant dysplasia. Patients treated after adolescence showed more stable late postoperative results.

Discussion: Hypertelorbitism is a clinical feature that may be present in various types of pathologies and in varying degrees of intensity. Many treatment options have been proposed over the past 50 years. The opportunity to watch and experience the evolution of these techniques made it possible to choose the most appropriate treatment for each patient's clinical characteristics.

Conclusion: Due to the variability of manifestation of hypertelorbitism, the massification of procedures and the establishment of treatment protocols are quite limited.



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How to Cite

Cardim VLN, Silva A. What the time has taught about Hyperteleorbitism. Arch Pediat Neurosurg [Internet]. 2022 May 9 [cited 2022 Aug. 17];4(2(May-August):e1242022. Available from: https://archpedneurosurg.com.br/pkp/index.php/sbnped2019/article/view/124